Chordoma is a rare, malignant bone tumor that develops from notochordal remnants along the spine, most often in the sacrum, skull base and mobile spine. Though relatively uncommon, affecting around 0,08 people per 100000 annually, chordomas make up about 4% of primary bone tumors. However, they present significant clinical difficulties due to their tendency to invade locally and their complex anatomy.
El cordoma es un tumor óseo raro, maligno, que se desarrolla a partir de remanentes no diferenciados de la notocorda a lo largo de la columna vertebral, más a menudo en la parte baja de la espalda, la base del cráneo y la columna vertebral móvil. Si bien es relativamente poco frecuente, con una incidencia de aproximadamente 0,08 personas por cada 100000 al año, los cordomas representan alrededor del 4% de los tumores óseos primarios y representan un gran desafío clínico debido a su capacidad de crecimiento local y a su anatomía compleja.
Transoral odontoidectomy (TO) is a surgical procedure employed to manage ventral compression of the cervicomedullary junction, frequently caused by tumors, infections or trauma. Among the neoplastic conditions requiring this approach, chordoma — a rare, malignant tumor arising from notochordal remnants — is of particular concern. This surgical approach allows for direct access to the anterior aspect of the odontoid process, enabling resection without extensive dissection of soft tissues and neurovascular structures.